Impaired Binding to Junctophilin-2 and Nanostructural Alteration in CPVT Mutation.
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Overview
abstract
published proceedings
author list (cited authors)
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Yin, L., Zahradnikova, A., Rizzetto, R., Boncompagni, S., Rabesahala de Meritens, C., Zhang, Y., ... Gmez, A. M.
complete list of authors
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Yin, Liheng||Zahradnikova, Alexandra||Rizzetto, Riccardo||Boncompagni, Simona||Rabesahala de Meritens, Camille||Zhang, Yadan||Joanne, Pierre||Marqués-Sulé, Elena||Aguilar-Sánchez, Yuriana||Fernández-Tenorio, Miguel||Villejoubert, Olivier||Li, Linwei||Wang, Yue Yi||Mateo, Philippe||Nicolas, Valérie||Gerbaud, Pascale||Lai, F Anthony||Perrier, Romain||Álvarez, Julio L||Niggli, Ernst||Valdivia, Héctor H||Valdivia, Carmen R||Ramos-Franco, Josefina||Zorio, Esther||Zissimopoulos, Spyros||Protasi, Feliciano||Benitah, Jean-Pierre||Gómez, Ana M
publisher
published in
Research
keywords
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Action Potential
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Action Potentials
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Animals
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Binding Sites
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Calcium
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Calcium Signaling
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Cells, Cultured
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HEK293 Cells
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Humans
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Junctophilin
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Membrane Proteins
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Mice
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Mice, Inbred C57BL
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Mutation
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Myocytes, Cardiac
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Polymorphic Catecholaminergic Ventricular Tachycardia
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Protein Binding
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Ryanodine Receptor
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Ryanodine Receptor Calcium Release Channel
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Tachycardia, Ventricular
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Ventricular Tachycardia
Identity
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Digital Object Identifier (DOI)
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URL
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https://doi.org/10.1161/circresaha.121.319094